ID:RFT1_HUMAN DESCRIPTION: RecName: Full=Protein RFT1 homolog; FUNCTION: May be involved in N-linked oligosaccharide assembly. May participate in the translocation of oligosaccharide from the cytoplasmic side to the lumenal side of the endoplasmic reticulum membrane. SUBCELLULAR LOCATION: Membrane; Multi-pass membrane protein (Potential). DISEASE: Defects in RFT1 are the cause of congenital disorder of glycosylation type 1N (CDG1N) [MIM:612015]. CDGs are a genetically heterogeneous group of autosomal recessive disorders caused by enzymatic defects in the synthesis and processing of asparagine (N)-linked glycans or oligosaccharides on glycoproteins. CDGs present with a wide variety of clinical features, such as disorders of the nervous system development, psychomotor retardation, dysmorphic features, hypotonia, coagulation disorders, and immunodeficiency. Type 1 CDGs comprise defects in the assembly of the dolichol lipid-linked oligosaccharide chain and its transfer to the nascent protein. These disorders can be identified by a characteristic abnormal isoelectric focusing profile of plasma transferrin. SIMILARITY: Belongs to the RFT1 family.
The RNAfold program from the Vienna RNA Package is used to perform the secondary structure predictions and folding calculations. The estimated folding energy is in kcal/mol. The more negative the energy, the more secondary structure the RNA is likely to have.
ModBase Predicted Comparative 3D Structure on Q96AA3
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Orthologous Genes in Other Species
Orthologies between human, mouse, and rat are computed by taking the best BLASTP hit, and filtering out non-syntenic hits. For more distant species reciprocal-best BLASTP hits are used. Note that the absence of an ortholog in the table below may reflect incomplete annotations in the other species rather than a true absence of the orthologous gene.
Cellular Component: GO:0005789 endoplasmic reticulum membrane GO:0016020 membrane GO:0016021 integral component of membrane
Descriptions from all associated GenBank mRNAs
AL713685 - Homo sapiens mRNA; cDNA DKFZp667J092 (from clone DKFZp667J092). KY814482 - Homo sapiens protein RFT1 homolog (RFT1) mRNA, complete cds. AK098811 - Homo sapiens cDNA FLJ25945 fis, clone JTH12731. JD513963 - Sequence 494987 from Patent EP1572962. JD524555 - Sequence 505579 from Patent EP1572962. JD352398 - Sequence 333422 from Patent EP1572962. JD223872 - Sequence 204896 from Patent EP1572962. JD150810 - Sequence 131834 from Patent EP1572962. JD541341 - Sequence 522365 from Patent EP1572962. JD119383 - Sequence 100407 from Patent EP1572962. JD150593 - Sequence 131617 from Patent EP1572962. JD525856 - Sequence 506880 from Patent EP1572962. JD413621 - Sequence 394645 from Patent EP1572962. JD107573 - Sequence 88597 from Patent EP1572962. JD505851 - Sequence 486875 from Patent EP1572962. JD356387 - Sequence 337411 from Patent EP1572962. JD505852 - Sequence 486876 from Patent EP1572962. JD398813 - Sequence 379837 from Patent EP1572962. JD070580 - Sequence 51604 from Patent EP1572962. JD422137 - Sequence 403161 from Patent EP1572962. JD463317 - Sequence 444341 from Patent EP1572962. JD213415 - Sequence 194439 from Patent EP1572962. JD407686 - Sequence 388710 from Patent EP1572962. JD152370 - Sequence 133394 from Patent EP1572962. JD258846 - Sequence 239870 from Patent EP1572962. JD353127 - Sequence 334151 from Patent EP1572962. JD513566 - Sequence 494590 from Patent EP1572962. JD523038 - Sequence 504062 from Patent EP1572962. JD361302 - Sequence 342326 from Patent EP1572962. JD157618 - Sequence 138642 from Patent EP1572962. JD524906 - Sequence 505930 from Patent EP1572962. JD420684 - Sequence 401708 from Patent EP1572962. JD199197 - Sequence 180221 from Patent EP1572962. JD257901 - Sequence 238925 from Patent EP1572962. JD090561 - Sequence 71585 from Patent EP1572962. JD239288 - Sequence 220312 from Patent EP1572962. JD536311 - Sequence 517335 from Patent EP1572962. JD459928 - Sequence 440952 from Patent EP1572962. JD410293 - Sequence 391317 from Patent EP1572962. JD232043 - Sequence 213067 from Patent EP1572962. JD370690 - Sequence 351714 from Patent EP1572962. JD422367 - Sequence 403391 from Patent EP1572962. JD399682 - Sequence 380706 from Patent EP1572962. JD392799 - Sequence 373823 from Patent EP1572962. BC101247 - Homo sapiens hypothetical locus LOC285398, mRNA (cDNA clone IMAGE:40023165). BC101248 - Homo sapiens hypothetical locus LOC285398, mRNA (cDNA clone IMAGE:40023166). BC101250 - Homo sapiens hypothetical locus LOC285398, mRNA (cDNA clone IMAGE:40023168). BC101249 - Homo sapiens hypothetical locus LOC285398, mRNA (cDNA clone IMAGE:40023167). BC113058 - Homo sapiens hypothetical locus LOC285398, mRNA (cDNA clone IMAGE:40023169). BC113059 - Homo sapiens hypothetical locus LOC285398, mRNA (cDNA clone IMAGE:40023170). JD043033 - Sequence 24057 from Patent EP1572962. JD161092 - Sequence 142116 from Patent EP1572962. JD324962 - Sequence 305986 from Patent EP1572962. JD500787 - Sequence 481811 from Patent EP1572962. JD051741 - Sequence 32765 from Patent EP1572962. JD197889 - Sequence 178913 from Patent EP1572962. KJ903577 - Synthetic construct Homo sapiens clone ccsbBroadEn_12971 RFT1 gene, encodes complete protein. JD482829 - Sequence 463853 from Patent EP1572962. JD345258 - Sequence 326282 from Patent EP1572962. JD064141 - Sequence 45165 from Patent EP1572962. JD291269 - Sequence 272293 from Patent EP1572962. JD102514 - Sequence 83538 from Patent EP1572962. BC043595 - Homo sapiens RFT1 homolog (S. cerevisiae), mRNA (cDNA clone MGC:50674 IMAGE:5769824), complete cds. JD384731 - Sequence 365755 from Patent EP1572962. JD457683 - Sequence 438707 from Patent EP1572962. JD324836 - Sequence 305860 from Patent EP1572962. JD315205 - Sequence 296229 from Patent EP1572962. JD363833 - Sequence 344857 from Patent EP1572962. JD301940 - Sequence 282964 from Patent EP1572962. JD174226 - Sequence 155250 from Patent EP1572962. JD231469 - Sequence 212493 from Patent EP1572962. JD344926 - Sequence 325950 from Patent EP1572962. JD042463 - Sequence 23487 from Patent EP1572962. JD095878 - Sequence 76902 from Patent EP1572962. JD328667 - Sequence 309691 from Patent EP1572962. JD501666 - Sequence 482690 from Patent EP1572962. JD115285 - Sequence 96309 from Patent EP1572962. JD171400 - Sequence 152424 from Patent EP1572962. JD526770 - Sequence 507794 from Patent EP1572962. BC006846 - Homo sapiens RFT1 homolog (S. cerevisiae), mRNA (cDNA clone IMAGE:3450968), partial cds. AJ318099 - Homo sapiens mRNA for putative endoplasmic reticulum multispan transmembrane protein (RFT1 gene). JD180976 - Sequence 162000 from Patent EP1572962. JD185108 - Sequence 166132 from Patent EP1572962. JD180841 - Sequence 161865 from Patent EP1572962. JD452090 - Sequence 433114 from Patent EP1572962. JD462305 - Sequence 443329 from Patent EP1572962.
Biochemical and Signaling Pathways
Reactome (by CSHL, EBI, and GO)
Protein Q96AA3 (Reactome details) participates in the following event(s):
R-HSA-446212 Flipping of the N-glycan precursor to inside the ER R-HSA-446193 Biosynthesis of the N-glycan precursor (dolichol lipid-linked oligosaccharide, LLO) and transfer to a nascent protein R-HSA-446203 Asparagine N-linked glycosylation R-HSA-597592 Post-translational protein modification R-HSA-392499 Metabolism of proteins